(R)-3-Hydroxyisobutyric acid |
| Catalog No.GC30661 |
(R)-3-하이드록시이소부티르산은 l-발린과 티민 경로의 중간체이며 매우 드문 유전성 대사 질환인 3-하이드록시이소부티르산뇨증과 메틸말론산 세미알데하이드 탈수소효소 결핍증의 진단에 중요한 역할을 합니다.
Products are for research use only. Not for human use. We do not sell to patients.
Cas No.: 1910-47-0
Sample solution is provided at 25 µL, 10mM.
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(R)-3-Hydroxyisobutyric acid is an intermediate in the pathways of l-valine and thymine and plays an important role in the diagnosis of the very rare inherited metabolic diseases 3-hydroxyisobutyric aciduria and methylmalonic semialdehyde dehydrogenase deficiency.
[1]. Podebrad F, et al. Stereodifferentiation of 3-hydroxyisobutyric- and 3-aminoisobutyric acid in human urine by enantioselective multidimensional capillary gas chromatography-mass spectrometry. Clin Chim Acta. 2000 Feb 25;292(1-2):93-105.
Average Rating: 5 (Based on Reviews and 14 reference(s) in Google Scholar.)
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