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Inicio >> Signaling Pathways >> Metabolism >> Inborn Errors of Metabolism

Inborn Errors of Metabolism

Products for  Inborn Errors of Metabolism

  1. Cat.No. Nombre del producto Información
  2. GC19941 DL-Leucic Acid DL-Leucic Acid Chemical Structure
  3. GC52404 γ-Glu-Phe (trifluoroacetate salt)

    γ-Glutamylphenylalanine

     A dipeptide with metabolism-altering activity γ-Glu-Phe (trifluoroacetate salt) Chemical Structure
  4. GC42051 1-β-D-Glucosylsphingosine (d18:1)

    Glucosyl-C18-Sphingosine, Glucosylsphingosine (d18:1), 1-β-D-Glucosylsphingosine (synthetic)

     1-β-D-Glucosylsphingosine is a glucosylsphingosine, which are deacetylated lysolipid derivatives of glucocerebrosides. 1-β-D-Glucosylsphingosine (d18:1) Chemical Structure
  5. GC18609 1-Deoxysphinganine (m18:0)

    1-deoxySA, ES-285, Spisulosine

     La 1-desoxiesfinganina (m18:0) (ES-285) es un compuesto antiproliferativo (antitumoral) de origen marino. La 1-desoxiesfinganina (m18:0) inhibe el crecimiento de las células prostÁticas PC-3 y LNCaP a través de la acumulaciÓn de ceramida intracelular y PKCζ activaciÓn. 1-Deoxysphinganine (m18:0) Chemical Structure
  6. GC41907 13C C16 Sphingomyelin (d18:1/16:0)

    Palmitoyl Sphingomyelin-13C, N-Palmitoyl-D-erythro-Sphingosylphosphorylcholine-13C, SM(d18:1/16:0-13C), Sphingomyelin (d18:1/16:0-13C)

     13C C16 Sphingomyelin is an isotopically enriched form of C16 sphingomyelin with carbon-13 occurring on the fatty acid portion. 13C C16 Sphingomyelin (d18:1/16:0) Chemical Structure
  7. GC52122 2’-Deoxyadenosine-5’-diphosphate (sodium salt)

    dADP, 2'-deoxy-ADP

     A nucleotide diphosphate 2’-Deoxyadenosine-5’-diphosphate (sodium salt) Chemical Structure
  8. GC45321 2',3',5'-Triacetyluridine   2',3',5'-Triacetyluridine Chemical Structure
  9. GC46540 2'-Deoxyadenosine-5'-triphosphate (sodium salt hydrate) A purine nucleotide 2'-Deoxyadenosine-5'-triphosphate (sodium salt hydrate) Chemical Structure
  10. GC49840 2-Methylbutyrylglycine

    2-MBG, N-sec-Valerylglycine

     A metabolite of isoleucine 2-Methylbutyrylglycine Chemical Structure
  11. GC52083 21-Deoxycortisone

    21-Desoxycortisone, NSC 38722

     A corticosteroid metabolite of 11-keto progesterone 21-Deoxycortisone Chemical Structure
  12. GC41614 24-dehydro Cholesterol

    Desmosterol

    El 24-deshidrocolesterol es una molécula similar al colesterol.

     24-dehydro Cholesterol Chemical Structure
  13. GC46243 24-dehydro Cholesterol-d6

    Desmosterol-d6

     An internal standard for the quantification of 24-dehydro cholesterol 24-dehydro Cholesterol-d6 Chemical Structure
  14. GC46068 3β-OH-7-Oxocholenic Acid

    3β-hydroxy-7-oxo-5-Cholenoic Acid, 3β-hydroxy-7-Oxochol-5-enoic Acid

     A bile acid 3β-OH-7-Oxocholenic Acid Chemical Structure
  15. GC46584 3-Aminoisobutyric Acid (sodium salt)

    β-Aminoisobutyric Acid, BAIBA

     A neuropeptide with diverse biological activities 3-Aminoisobutyric Acid (sodium salt) Chemical Structure
  16. GC42292 3-Hydroxypropionic Acid (sodium salt)

    Sodium β-hydroxypropionate

     3-Hydroxypropionic acid is a building block in the synthesis of a variety of compounds with industrial applications, including acrylic acid, acrylamide, and 1,3-propanediol. 3-Hydroxypropionic Acid (sodium salt) Chemical Structure
  17. GC49149 3-Methylglutaconic Acid

    β-Methylglutaconic Acid, 3-MGA, 3-MGC Acid, NSC 249232

     A branched-chain organic acid 3-Methylglutaconic Acid Chemical Structure
  18. GC41582 4(Z),7(Z)-Decadienoic Acid 4(Z),7(Z)-Decadienoic acid is a polyunsaturated fatty acid (PUFA). 4(Z),7(Z)-Decadienoic Acid Chemical Structure
  19. GC42445 4-Methylumbelliferyl β-D-Galactopyranoside-6-sulfate (sodium salt)

    4-MU β-D-galactopyranoside-6-sulfate, 4-Methylumbelliferyl Gal-6S, 4-MU-Gal-6S

     El 4-metilumbeliferil β-D-galactopiranÓsido-6-sulfato (sal de sodio) es un tinte fluorescente. 4-Methylumbelliferyl β-D-Galactopyranoside-6-sulfate (sodium salt) Chemical Structure
  20. GC42442 4-Methylumbelliferyl 2-sulfamino-2-deoxy-α-D-Glucopyranoside (sodium salt)

    4-MU-α-GlcNS

     El 4-metilumbeliferil 2-sulfamino-2-desoxi-α-D-glucopiranÓsido (sal de sodio) es un sustrato fluorogénico de la heparina sulfamidasa, se desulfura en 4-MU-α-GlcNH2. 4-Methylumbelliferyl 2-sulfamino-2-deoxy-α-D-Glucopyranoside (sodium salt) Chemical Structure
  21. GC40510 4-Methylumbelliferyl-α-D-Galactopyranoside

    MU-α-Gal, 4-MU-α-Gal

     El 4-metilumbeliferil-α-D-galactopiranÓsido (4MU-α-Gal), un sustrato para la α-galactosidasa A (GLA), es un sustrato azul profluorogénico. 4-Methylumbelliferyl-α-D-Galactopyranoside Chemical Structure
  22. GC19852 4-Methylumbelliferyl-α-D-glucopyranoside

    4-Methylumbelliferyl-α-D-Glucose, 4-Methylumbelliferyl-α-D-Glucoside, 4-MU-α-D-Glucopyranoside

     4-Methylumbelliferyl-α-D-glucopyranoside Chemical Structure
  23. GC11870 4-Methylumbelliferyl-β-D-Glucopyranoside

    4-MU-GLU;4-MU-β-Gluc;4-MUG;MU-GLU

     4-Methylumbelliferyl-β-D-Glucopyranoside, un β-D-glucoside, es un sustrato fluorogénico para β-glucosidasa, se utiliza para analizar la actividad de β-glucosidasa. 4-Methylumbelliferyl-β-D-Glucopyranoside Chemical Structure
  24. GC49499 5(Z)-Dodecenoic Acid

    C12:1 n-7, C12:1(5Z), cis-5-Dodecenoic Acid

     El Ácido 5(Z)-dodecenoico es un metabolito endÓgeno con actividades inhibitorias contra COX-I y COX-II. 5(Z)-Dodecenoic Acid Chemical Structure
  25. GC46735 7-Biopterin

    Primapterin, L-Primapterin

     A pterin 7-Biopterin Chemical Structure
  26. GC46242 7-dehydro Cholesterol-d7

    Provitamin D3-d7

    7-dehydro Cholesterol (7-DHC) is an immediate precursor of cholesterol

     7-dehydro Cholesterol-d7 Chemical Structure
  27. GC42695 Acetoacetyl Coenzyme A (sodium salt hydrate)

    Acetoacetyl-CoA

    Acetoacetyl coenzyme A (acetoacetyl-CoA) is a precursor to HMG-CoA in the isoprenoid pathway.

     Acetoacetyl Coenzyme A (sodium salt hydrate) Chemical Structure
  28. GC46083 Adenylosuccinic Acid

    Aspartyl Adenylate

    El ácido adenylosuccínico es un nucleótido de purina y un intermediario en el ciclo de los nucleótidos de purina.

     Adenylosuccinic Acid Chemical Structure
  29. GC42963 BODIPY-C12 Ceramide (d18:1/12:0)

    BODIPY-C12 Ceramide, BODIPY-Ceramide (d18:1/12:0), BODIPY-Cer(d18:1/12:0), BODIPY-N-Lauroyl-D-erythro-Sphingosine, B12Cer

     BODIPY-C12 Ceramide (B12Cer) is a fluorescently-tagged form of C12 ceramide that displays excitation/emission maxima of 505/540 nm, respectively. BODIPY-C12 Ceramide (d18:1/12:0) Chemical Structure
  30. GC43006 C12 Ceramide (d18:1/12:0)

    Cer(d18:1/12:0), C12 Ceramide, Ceramide (d18:1/12:0), N-Lauroyl-D-erythro-Sphingosine

     La ceramida C12 (d18:1/12:0) (N-lauroil-D-eritro-esfingosina), una ceramida natural, se forma por hidrÓlisis de la esfingomielina C12. C12 Ceramide (d18:1/12:0) Chemical Structure
  31. GC43032 C16 Globotriaosylceramide (d18:1/16:0)

    C16 Ceramide Trihexoside (d18:1/16:0), Gb3 (d18:1/16:0), N-Hexadecanoyl-ceramide trihexoside

     C16 globotriaosylceramide is an endogenous sphingolipid found in mammalian cell membranes that is synthesized from C16 lactosylceramide. C16 Globotriaosylceramide (d18:1/16:0) Chemical Structure
  32. GC46980 C16 Globotriaosylceramide-d9 (d18:1/16:0-d9)

    C16 Ceramide Trihexoside (d18:1/16:0-d9), Gb3 (d18:1/16:0-d9), N-Hexadecanoyl-d9 (13,13,14,14,15,15,16,16,16)-ceramide Trihexoside

     A neuropeptide with diverse biological activities C16 Globotriaosylceramide-d9 (d18:1/16:0-d9) Chemical Structure
  33. GC43033 C16 Lactosylceramide (d18:1/16:0)

    N-Hexadecanoyl Lactosylceramide, LacCer(d18:1/16:0), Lactosylceramide (d18:1/16:0), C16 Lactosyl(β) Ceramide (d18:1/16:0)

     C16 Lactosylceramide is an endogenous bioactive sphingolipid. C16 Lactosylceramide (d18:1/16:0) Chemical Structure
  34. GC46982 C16 Lactosylceramide-d3 (d18:1/16:0-d3)

    C16 Lactosyl(β) Ceramide-d3 (d18:1/16:0-d3), LacCer(d18:1/16:0-d3), Lactosylceramide-d3 (d18:1/16:0-d3), N-ω-CD3-Hexadecanoyl-lactosylceramide, N-Hexadecanoyl Lactosylceramide-d3

     A neuropeptide with diverse biological activities C16 Lactosylceramide-d3 (d18:1/16:0-d3) Chemical Structure
  35. GC43035 C16 Sphingomyelin (d18:1/16:0)

    Palmitoyl Sphingomyelin, N-Palmitoyl-D-erythro-Sphingosylphosphorylcholine, SM(d18:1/16:0), Sphingomyelin (d18:1/16:0)

     Sphingomyelins are complex membrane lipids composed of phosphorylcholine, sphingosine, and an acylated group, such as a fatty acid. C16 Sphingomyelin (d18:1/16:0) Chemical Structure
  36. GC45661 C16 Sphingomyelin-d9 (d18:1/16:0-d9)

    Palmitoyl Sphingomyelin-d9

     A neuropeptide with diverse biological activities C16 Sphingomyelin-d9 (d18:1/16:0-d9) Chemical Structure
  37. GC43038 C17 Ceramide (d18:1/17:0)

    Cer(d18:1/17:0), Ceramide (d18:1/17:0), N-heptadecanoyl-D-erythro-Sphingosine

     C17 Ceramide is a synthetic ceramide that contains a non-natural C17:0 fatty acid acylated to sphingosine. C17 Ceramide (d18:1/17:0) Chemical Structure
  38. GC43041 C17 Globotriaosylceramide (d18:1/17:0)

    C17 Ceramide Trihexoside (d18:1/17:0), N-Heptadecanoyl Ceramide Trihexoside

     C17 Globotriaosylceramide is a sphingolipid that has been used as an internal standard for the quantification of globotriaosylceramides in plasma and urine from patients with Fabry disease by GC-MS. C17 Globotriaosylceramide (d18:1/17:0) Chemical Structure
  39. GC46985 C18 3'-sulfo Galactosylceramide-d3 (d18:1/18:0-d3)

    N-Octadecanoyl Sulfatide-d3, N-ω-CD3-Octadecanoyl-sulfatide

     A neuropeptide with diverse biological activities C18 3'-sulfo Galactosylceramide-d3 (d18:1/18:0-d3) Chemical Structure
  40. GC43049 C18 Globotriaosylceramide (d18:1/18:0)

    C18 Ceramide Trihexoside (d18:1/18:0), Gb3(d18:1/18:0), N-Octadecanoyl-ceramide trihexoside

     C18 globotriaosylceramide is an endogenous sphingolipid found in mammalian cell membranes that is synthesized from lactosylceramide. C18 Globotriaosylceramide (d18:1/18:0) Chemical Structure
  41. GC46995 C18 Globotriaosylceramide-d3 (d18:1/18:0-d3)

    N-ω-CD3-Octadecanoyl-ceramide Trihexoside, Galα1-4Galβ1-4Glcβ-Cer(d18:1/18:0) d3, Gb3(d18:1/18:0-d3), Globotriaosylceramide-d3 (d18:1/18:0-d3)

     A neuropeptide with diverse biological activities C18 Globotriaosylceramide-d3 (d18:1/18:0-d3) Chemical Structure
  42. GC43059 C2 Adamantanyl Galactosylceramide (d18:1/2:0)

    C2 Adamantanyl Galactosylceramide (d18:1/2:0) (AdaGalCer) is a bioactive sphingolipid.

     C2 Adamantanyl Galactosylceramide (d18:1/2:0) Chemical Structure
  43. GC43068 C20 Sphingomyelin (d18:1/20:0)

    N-eicosanoyl-D-erythro-Sphingosylphosphorylcholine, SM(d18:1/20:0)

     C20 Sphingomyelin is a naturally occurring sphingolipid. C20 Sphingomyelin (d18:1/20:0) Chemical Structure
  44. GC40041 Cholesteryl Lignocerate

    24:0 CE, 24:0 Cholesterol ester

     Cholesteryl lignocerate is a cholesterol ester that has been found in human meibum. Cholesteryl Lignocerate Chemical Structure
  45. GC47115 Coenzyme B12 (hydrate)

    Adenosylcobalamin, AdoCbl, Cobamamide, Dibenzcozamide, LM-176

     A neuropeptide with diverse biological activities Coenzyme B12 (hydrate) Chemical Structure
  46. GC47189 D-erythro/L-threo Lysosphingomyelin (d18:1)

    D-erythro/L-threo Lyso SM(18:1), D-erythro/L-threo Sphingosine-1-Phosphocholine (d18:1), D-erythro/L-threo-Sphingosylphosphorylcholine

     A mixture of bioactive sphingolipids D-erythro/L-threo Lysosphingomyelin (d18:1) Chemical Structure
  47. GC47204 D-Fructose-13C6

    D-(-)-Fructose-13C6, D-(-)-Levulose-13C6

     An internal standard for the quantification of D-fructose D-Fructose-13C6 Chemical Structure
  48. GC49325 Dihydroxyacetone Phosphate (magnesium salt hydrate)

    DHAP, Glycerone Phosphate

     A glycerolipid precursor Dihydroxyacetone Phosphate (magnesium salt hydrate) Chemical Structure
  49. GC43486 DL-Cystathionine (hydrochloride)

    DL-Allocystathionine

     DL-Cystathionine is an intermediate in the synthesis of cysteine that is produced from homocysteine and serine by the action of cystathionine-β-synthase (CBS). DL-Cystathionine (hydrochloride) Chemical Structure
  50. GC47286 Eliglustat-d15 (tartrate)

    Genz 99067-d15 tartrate

     An internal standard for the quantification of eliglustat Eliglustat-d15 (tartrate) Chemical Structure
  51. GC18469 Galactosylcerebrosides (bovine)

    Galactosylcerebroside, Cerebroside, Ganglioside GL1b

     Galactosylcerebrosides are glycosphingolipids that contain a galactose attached to a ceramide acylated with hydroxy and non-hydroxy fatty acids. Galactosylcerebrosides (bovine) Chemical Structure
  52. GC43721 Galactosylcerebrosides (hydroxy)

    Cerebrosides; Phrenosin (bottom spot)

     Galactosylcerebrosides are glycosphingolipids that contain a galactose attached to a ceramide acylated with a hydroxy or non-hydroxy fatty acid. Galactosylcerebrosides (hydroxy) Chemical Structure
  53. GC43722 Galactosylcerebrosides (non-hydroxy)

    Cerebrosides; Kerasin (top spot)

     Galactosylcerebrosides are glycosphingolipids that contain a galactose attached to a ceramide acylated with a hydroxy or non-hydroxy fatty acid. Galactosylcerebrosides (non-hydroxy) Chemical Structure
  54. GC43723 Galactosylsphingosine (d18:1)

    Galactosylsphingosine, Psychosine

     La galactosilesfingosina (d18:1) (galactosilesfingosina), un sustrato de la enzima galactocerebrosidasa (GALC), es un biomarcador potencial de la enfermedad de Krabbe. Galactosylsphingosine (d18:1) Chemical Structure
  55. GC43727 Ganglioside GD1a mixture (sodium salt)

    Ganglioside B1

    Ganglioside GD1a is a sialic acid-containing glycosphingolipid found in brain, erythrocytes, bone marrow, testis, spleen, and liver.

     Ganglioside GD1a mixture (sodium salt) Chemical Structure
  56. GC47392 Ganglioside GM1 Mixture (ovine) (ammonium salt)

    GM1, Monosialoganglioside GM1

     A mixture of ganglioside GM1 Ganglioside GM1 Mixture (ovine) (ammonium salt) Chemical Structure
  57. GC47393 Ganglioside GM1 Mixture (porcine brain) (ammonium salt)

    GM1, Monosialoganglioside GM1

     A mixture of ganglioside GM1 Ganglioside GM1 Mixture (porcine brain) (ammonium salt) Chemical Structure
  58. GC40016 Ganglioside GM2 Mixture (sodium salt)

    GM2 Mixture, Monosialoganglioside GM2 Mixture

     Ganglioside GM2 is a glycosphingolipid component of cellular membranes, primarily the plasma membrane. Ganglioside GM2 Mixture (sodium salt) Chemical Structure
  59. GC52492 Globotriaosylceramide (hydroxy) (porcine RBC)

    Ceramide Trihexosides (bottom spot) (porcine)

     A sphingolipid Globotriaosylceramide (hydroxy) (porcine RBC) Chemical Structure
  60. GC52491 Globotriaosylceramide (non-hydroxy) (porcine RBC)

    Ceramide Trihexosides (top spot) (porcine)

     A sphingolipid Globotriaosylceramide (non-hydroxy) (porcine RBC) Chemical Structure
  61. GC43758 Globotriaosylceramides (hydroxy) (porcine) Globotriaosycleramides are glycosphingolipids found in mammalian cell membranes that are synthesized from lactosylceramides. Globotriaosylceramides (hydroxy) (porcine) Chemical Structure
  62. GC43760 Globotriaosylceramides (porcine)

    Ceramide Trihexosides (porcine)

     Globotriaosycleramides are glycosphingolipids found in mammalian cell membranes that are synthesized from lactosylceramides. Globotriaosylceramides (porcine) Chemical Structure
  63. GC43768 Glucocerebrosides (Gaucher's spleen)

    Ganglioside GL1a, Gaucher cerebroside, GluCers (Gaucher's spleen), Glucocerebrosides, Glucosylceramides (Gaucher's spleen)

     Glucocerebrosides are formed by the tethering of glucose to a ceramide by glucosylceramide synthase. Glucocerebrosides (Gaucher's spleen) Chemical Structure
  64. GC52493 Glucosylceramide (bovine buttermilk)

    GluCers (buttermilk), Glucocerebrosides (buttermilk)

     A sphingolipid Glucosylceramide (bovine buttermilk) Chemical Structure
  65. GC52219 Heptadecanoyl-L-carnitine (chloride)

    CAR 17:0, C17:0 Carnitine, L-Carnitine heptadecanoyl ester, L-Heptadecanoylcarnitine

     A long-chain acylcarnitine Heptadecanoyl-L-carnitine (chloride) Chemical Structure
  66. GC52231 Heptadecanoyl-L-carnitine-d3 (chloride)

    CAR 17:0-d3, C17:0 Carnitine-d3, L-Carnitine heptadecanoyl ester-d3, L-Heptadecanoylcarnitine-d3

     An internal standard for the quantification of heptadecanoyl-L-carnitine Heptadecanoyl-L-carnitine-d3 (chloride) Chemical Structure
  67. GC49678 Heptadecanoyl-L-carnitine-d3 (chloride) MaxSpec® Standard

    CAR 17:0-d3, C17:0 Carnitine-d3, L-Carnitine heptadecanoyl ester-d3, L-Heptadecanoylcarnitine-d3

     A quantitative analytical standard guaranteed to meet MaxSpec® identity, purity, stability, and concentration specifications Heptadecanoyl-L-carnitine-d3 (chloride) MaxSpec® Standard Chemical Structure
  68. GC49479 Hypoxanthine-d4

    6-Hydroxypurine-d4

     An internal standard for the quantification of hypoxanthine Hypoxanthine-d4 Chemical Structure
  69. GC43914 Isobutyryl Coenzyme A (sodium salt)

    Isobutyryl-CoA

     Isobutyryl coenzyme A (isobutyryl-CoA) is a short-chain branched acyl CoA. Isobutyryl Coenzyme A (sodium salt) Chemical Structure
  70. GC52009 Isovaleryl-DL-carnitine-d9 (chloride)

    CAR 5:0-d9, C5:0 Carnitine-d9, DL-Carnitine isovaleryl ester-d9, DL-Isovalerylcarnitine-d9

     An internal standard for the quantification of isovaleryl-DL-carnitine Isovaleryl-DL-carnitine-d9 (chloride) Chemical Structure
  71. GC52323 L-Isoleucine-13C6

    L-(+)-Isoleucine-13C6

     An internal standard for the quantification of L-isoleucine L-Isoleucine-13C6 Chemical Structure
  72. GC49782 L-Phenylalanine-13C6

    (-)-Phenylalanine-13C6

     L-fenilalanina-13C6 ((S)-2-amino-3-fenilpropiÓnico Ácido-13C6) es la L-fenilalanina marcada con 13C. L-Phenylalanine-13C6 Chemical Structure
  73. GC44101 Lyso-Globotriaosylceramide (d18:1)

    Globotriaosylsphingosine (d18:1), Lyso-Ceramide Trihexoside, Lyso-Gb3

     Lyso-globotriaosylceramide is a form of globotriaosylceramide that is lacking the fatty acyl group. Lyso-Globotriaosylceramide (d18:1) Chemical Structure
  74. GC48345 Lyso-Monosialoganglioside GM2 (ammonium salt)

    Lysoganglioside GM2, Lyso-GM2, lyso-Monosialoganglioside GM2

     Lyso-Monosialoganglioside GM2 (ammonium salt) Chemical Structure
  75. GC44105 Lysosphingomyelin (d18:1)

    D-erythro Lyso SM(18:1), D-erythro-Sphingophosphorylcholine, D-erythro Sphingosine-1-Phosphocholine (d18:1), Lyso-SM(d18:1), Lysosphingomyelin (d18:1)

     Sphingomyelins are complex membrane lipids composed of phosphorylcholine, sphingosine, and an acylated group, such as a fatty acid. Lysosphingomyelin (d18:1) Chemical Structure
  76. GC19926 Methyl malonic acid

    Dimethyl Malonate; Malonic Acid Dimethyl Ester; Methyl Malonate

     Methyl malonic acid Chemical Structure
  77. GC49472 Methylmalonic Acid-d3

    Isosuccinic Acid-d3, Methylmalonate-d3, MMA-d3

     El Ácido metilmalÓnico-d3 (Ácido metilpropanodioico-d3) es el Ácido metilmalÓnico marcado con deuterio. El Ácido metilmalÓnico (metilmalonato) es un indicador de la deficiencia de vitamina B-12 en el cÁncer. Methylmalonic Acid-d3 Chemical Structure
  78. GC49246 N-(3-Phenylpropionyl)glycine An acylglycine N-(3-Phenylpropionyl)glycine Chemical Structure
  79. GC49388 N-Butyldeoxynojirimycin-d9 (hydrochloride)

    Miglustat-d9, NB-DNJ-d9

     An internal standard for the quantification of N-butyldeoxynojirimycin N-Butyldeoxynojirimycin-d9 (hydrochloride) Chemical Structure
  80. GC49240 N-Propionylglycine

    NSC 158539

     A glycine-conjugated form of propionic acid N-Propionylglycine Chemical Structure
  81. GC47779 Nitisinone-13C6

    NTBC-13C6

     An internal standard for the quantification of nitisinone Nitisinone-13C6 Chemical Structure
  82. GC49323 Norcholic Acid

    23-Norcholic Acid

     El Ácido norcÓlico es un Ácido biliar C23 minorbile normal que tiene cuatro cadenas laterales y existe en la orina humana y el meconio. Norcholic Acid Chemical Structure
  83. GC46187 Norhyodeoxycholic Acid

    3α,6α-Dihydroxy-24-nor-5β-cholan-23-oic Acid, NHDCA

     A synthetic bile acid Norhyodeoxycholic Acid Chemical Structure
  84. GC46192 Octanoic Acid-13C

    Caprylic Acid-13C

     El Ácido octanoico-13C (Ácido caprÍlico-13C) es el Ácido octanoico marcado con 13C. Octanoic Acid-13C Chemical Structure
  85. GC45982 Octanoic Acid-d15

    Caprylic Acid-d15

     An internal standard for the quantification of octanoic acid Octanoic Acid-d15 Chemical Structure
  86. GC45996 Octanoic Acid-d2

    Caprylic Acid-d2

     An internal standard for the quantification of octanoic acid Octanoic Acid-d2 Chemical Structure
  87. GC45813 Octanoic Acid-d3

    Caprylic Acid-d3

     An internal standard for the quantification of octanoic acid Octanoic Acid-d3 Chemical Structure
  88. GC44488 Octanoyl Coenzyme A (sodium salt)

    Octanoyl-CoA

     Octanoyl coenzyme A (octanoyl-CoA) is a medium-chain acyl CoA and a metabolic intermediate in mitochondrial fatty acid β-oxidation. Octanoyl Coenzyme A (sodium salt) Chemical Structure
  89. GC44639 phytanoyl-Coenzyme A (triethylammonium salt)

    Phytanic Acid Coenzyme A Ester (triethylammonium salt), phytanoyl-CoA (triethylammonium salt)

     Phytanic acid is a saturated 20-carbon branched-chain fatty acid that can only be derived from dietary sources. phytanoyl-Coenzyme A (triethylammonium salt) Chemical Structure
  90. GC48724 Pregnanetriol

    NSC 52760, 5β-Pregnane-3α,17α,20α-triol

     A metabolite of 17α-hydroxyprogesterone Pregnanetriol Chemical Structure
  91. GC45981 Pristanic Acid-d3

    An internal standard for the quantification of pristanic acid

     Pristanic Acid-d3 Chemical Structure
  92. GC46215 S-Acetyl-L-glutathione

    S-Acetylglutathione

     A derivative of glutathione S-Acetyl-L-glutathione Chemical Structure
  93. GC52496 Sulfatide (bovine) (sodium salt)

    Galactosylceramide I3-sulfate, Ganglioside SM4, I3SO3-GalCer, SM4, Sulfated Galactocerebroside, 3-O-Sulfogalactosylceramide

     A mixture of isolated bovine sulfatides Sulfatide (bovine) (sodium salt) Chemical Structure
  94. GC44968 Sulfatides (bovine) (sodium salt) Sulfatides are endogenous sulfoglycolipids with various biological activities in the central and peripheral nervous systems, pancreas, and immune system. Sulfatides (bovine) (sodium salt) Chemical Structure
  95. GC40341 Tetrahydro-11-deoxy Cortisol

    NSC 53901, 5β-Pregnane-3α,17α,21-triol-20-one, Tetrahydrodeoxycortisol, THS

     Tetrahydro-11-deoxy cortisol (THS) is the primary urinary metabolite of 11-deoxycortisol. Tetrahydro-11-deoxy Cortisol Chemical Structure
  96. GC91083 Tiopronin-Cysteine Disulfide

    Un metabolito de tiopronina.

     Tiopronin-Cysteine Disulfide Chemical Structure
  97. GC45945 Trihydroxycholestanoic Acid

    Trihydroxycoprostanic Acid

     A cholic acid intermediate Trihydroxycholestanoic Acid Chemical Structure
  98. GC49328 UDP-α-D-Galactose (sodium salt)

    UDP-Gal, Uridine-5'-diphosphate-α-D-Galactose

     A nucleotide sugar UDP-α-D-Galactose (sodium salt) Chemical Structure
  99. GC26265 α-Hydroxyglutaric acid disodium

    2-Hydroxyglutarate disodium; 2-Hydroxyglutaric acid disodium; 2-Hydroxypentanedioic acid disodium

    α-Hydroxyglutaric acid (2-Hydroxyglutarate) disodium is an α-hydroxy acid form of glutaric acid. 

     α-Hydroxyglutaric acid disodium Chemical Structure

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