Inborn Errors of Metabolism
Products Related to Inborn Errors of Metabolism(96)
- GC45996Octanoic Acid-d2CAS: 64118-36-1Purity: >99.00%
An internal standard for the quantification of octanoic acid
- GC46083Adenylosuccinic AcidCAS: 19046-78-7Purity: >95.00%
Adenylosuccinic acid is a purine nucleotide and an intermediate in the purine nucleotide cycle.
- GC46192Octanoic Acid-13CCAS: 59669-16-8Purity: >98.00%
An internal standard for the quantification of octanoic acid
- GC462427-dehydro Cholesterol-d7CAS: 388622-58-0Purity: >99.00%
7-dehydro Cholesterol (7-DHC) is an immediate precursor of cholesterol
- GC4624324-dehydro Cholesterol-d6CAS: 1246298-67-8Purity: >99.00%
An internal standard for the quantification of 24-dehydro cholesterol
- GC465843-Aminoisobutyric Acid (sodium salt)CAS: 84796-61-2Purity: >95.00%
A neuropeptide with diverse biological activities
- GC46980C16 Globotriaosylceramide-d9 (d18:1/16:0-d9)CAS: 2738376-84-4Purity: >99.00%
A neuropeptide with diverse biological activities
- GC46982C16 Lactosylceramide-d3 (d18:1/16:0-d3)Purity: >99.00%
A neuropeptide with diverse biological activities
- GC46985C18 3'-sulfo Galactosylceramide-d3 (d18:1/18:0-d3)Purity: >99.00%
A neuropeptide with diverse biological activities
- GC46995C18 Globotriaosylceramide-d3 (d18:1/18:0-d3)Purity: >99.00%
A neuropeptide with diverse biological activities
- GC47189D-erythro/L-threo Lysosphingomyelin (d18:1)CAS: 82970-80-7Purity: >98.00%
A mixture of bioactive sphingolipids
- GC47204D-Fructose-13C6CAS: 201595-65-5Purity: >99.00%
D-Fructose-13C6, a 13 C-labeled D-Fructose, acts as an internal reference for fructose and xylitol quantitation.
- GC47286Eliglustat-d15 (tartrate)CAS: 1884556-84-6Purity: >99.00%
An internal standard for the quantification of eliglustat
- GC47392Ganglioside GM1 Mixture (ovine) (ammonium salt)CAS: 1007119-81-4Purity: >98.00%
A mixture of ganglioside G M1
- GC47393Ganglioside GM1 Mixture (porcine brain) (ammonium salt)CAS: 1007119-81-4Purity: >98.00%
A mixture of ganglioside G M1
- GC47779Nitisinone-13C6CAS: 1246815-63-3Purity: >98.00%
An internal standard for the quantification of nitisinone
| Catalog No. | Product Name | CAS No. | Purity | Structure |
|---|---|---|---|---|
| GC45996 | Octanoic Acid-d2 | 64118-36-1 | >99.00% | |
An internal standard for the quantification of octanoic acid | ||||
| GC46068 | 3β-OH-7-Oxocholenic Acid | 25218-38-6 | >98.00% | |
A bile acid | ||||
| GC46083 | Adenylosuccinic Acid | 19046-78-7 | >95.00% | |
Adenylosuccinic acid is a purine nucleotide and an intermediate in the purine nucleotide cycle. | ||||
| GC46187 | Norhyodeoxycholic Acid | 77518-23-1 | >98.00% | |
A synthetic bile acid | ||||
| GC46192 | Octanoic Acid-13C | 59669-16-8 | >98.00% | |
An internal standard for the quantification of octanoic acid | ||||
| GC46215 | S-Acetyl-L-glutathione | 3054-47-5 | >98.00% | |
A derivative of glutathione | ||||
| GC46242 | 7-dehydro Cholesterol-d7 | 388622-58-0 | >99.00% | |
7-dehydro Cholesterol (7-DHC) is an immediate precursor of cholesterol | ||||
| GC46243 | 24-dehydro Cholesterol-d6 | 1246298-67-8 | >99.00% | |
An internal standard for the quantification of 24-dehydro cholesterol | ||||
| GC46540 | 2'-Deoxyadenosine-5'-triphosphate (sodium salt hydrate) | - | >95.00% | |
A purine nucleotide | ||||
| GC46584 | 3-Aminoisobutyric Acid (sodium salt) | 84796-61-2 | >95.00% | |
A neuropeptide with diverse biological activities | ||||
| GC46735 | 7-Biopterin | 2636-52-4 | >98.00% | |
A pterin | ||||
| GC46980 | C16 Globotriaosylceramide-d9 (d18:1/16:0-d9) | 2738376-84-4 | >99.00% | |
A neuropeptide with diverse biological activities | ||||
| GC46982 | C16 Lactosylceramide-d3 (d18:1/16:0-d3) | - | >99.00% | |
A neuropeptide with diverse biological activities | ||||
| GC46985 | C18 3'-sulfo Galactosylceramide-d3 (d18:1/18:0-d3) | - | >99.00% | |
A neuropeptide with diverse biological activities | ||||
| GC46995 | C18 Globotriaosylceramide-d3 (d18:1/18:0-d3) | - | >99.00% | |
A neuropeptide with diverse biological activities | ||||
| GC47115 | Coenzyme B12 (hydrate) | - | >95.00% | |
A neuropeptide with diverse biological activities | ||||
| GC47189 | D-erythro/L-threo Lysosphingomyelin (d18:1) | 82970-80-7 | >98.00% | |
A mixture of bioactive sphingolipids | ||||
| GC47204 | D-Fructose-13C6 | 201595-65-5 | >99.00% | |
D-Fructose-13C6, a 13 C-labeled D-Fructose, acts as an internal reference for fructose and xylitol quantitation. | ||||
| GC47286 | Eliglustat-d15 (tartrate) | 1884556-84-6 | >99.00% | |
An internal standard for the quantification of eliglustat | ||||
| GC47392 | Ganglioside GM1 Mixture (ovine) (ammonium salt) | 1007119-81-4 | >98.00% | |
A mixture of ganglioside G M1 | ||||
| GC47393 | Ganglioside GM1 Mixture (porcine brain) (ammonium salt) | 1007119-81-4 | >98.00% | |
A mixture of ganglioside G M1 | ||||
| GC47779 | Nitisinone-13C6 | 1246815-63-3 | >98.00% | |
An internal standard for the quantification of nitisinone | ||||
| GC48345 | Lyso-Monosialoganglioside GM2 (ammonium salt) | - | >98.00% | |
| GC48724 | Pregnanetriol | 1098-45-9 | >95.00% | |
A metabolite of 17α-hydroxyprogesterone | ||||
