Heptadecanoyl-L-carnitine-d3 (chloride) (Synonyms: CAR 17:0-d3, C17:0 Carnitine-d3, L-Carnitine heptadecanoyl ester-d3, L-Heptadecanoylcarnitine-d3) |
رقم الكتالوجGC52231 |
An internal standard for the quantification of heptadecanoyl-L-carnitine
Products are for research use only. Not for human use. We do not sell to patients.
Sample solution is provided at 25 µL, 10mM.
Heptadecanoyl-L-carnitine-d3 is intended for use as an internal standard for the quantification of heptadecanoyl-L-carnitine by GC- or LC-MS. Heptadecanoyl-L-carnitine is a long-chain acylcarnitine composed of heptadecanoic acid and L-carnitine . Levels of heptadecanoyl-L-carnitine are increased in dried blood spots from neonates with propionic or methylmalonic acidemias, inborn errors of metabolism characterized by a deficiency in the activity of propionyl-CoA carboxylase or L-methylmalonyl-CoA mutase or its cofactor 5-deoxyadenosylcobalamin, respectively.1
1.Malvagia, S., Haynes, C.A., Grisotto, L., et al.Heptadecanoylcarnitine (C17) a novel candidate biomarker for propionic and methylmalonic acidemias during expanded newborn screeningClin. Chim. Acta450342-348(2015)
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