(R)-3-Hydroxyisobutyric acid |
Catalog No.GC30661 |
El Ácido (R)-3-hidroxiisobutÍrico es un intermediario en las vÍas de la l-valina y la timina y desempeÑa un papel importante en el diagnÓstico de las muy raras enfermedades metabÓlicas hereditarias aciduria 3-hidroxiisobutÍrica y deficiencia de metilmalÓnico semialdehÍdo deshidrogenasa.
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Cas No.: 1910-47-0
Sample solution is provided at 25 µL, 10mM.
(R)-3-Hydroxyisobutyric acid is an intermediate in the pathways of l-valine and thymine and plays an important role in the diagnosis of the very rare inherited metabolic diseases 3-hydroxyisobutyric aciduria and methylmalonic semialdehyde dehydrogenase deficiency.
[1]. Podebrad F, et al. Stereodifferentiation of 3-hydroxyisobutyric- and 3-aminoisobutyric acid in human urine by enantioselective multidimensional capillary gas chromatography-mass spectrometry. Clin Chim Acta. 2000 Feb 25;292(1-2):93-105.
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