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Glutarylcarnitine

Catalog No.GC31609

La glutarylcarnitine est le métabolite diagnostique de l'acidurie malonique et de l'acidurie glutarique de type I surveillée dans la plupart des programmes de dépistage néonatal par spectrométrie de masse en tandem.

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Glutarylcarnitine Chemical Structure

Cas No.: 102636-82-8

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Sample solution is provided at 25 µL, 10mM.

Description Chemical Properties Product Documents Related Products

Glutarylcarnitine is the diagnostic metabolite for malonic aciduria and glutaric aciduria type I monitored in most tandem mass spectrometry newborn screening programmes.

Malonylcarnitine and Glutarylcarnitine are important diagnostic metabolites in the screening of dried blood spots by tandem mass spectrometry[1].

[1]. Johnson DW, et al. Stability of malonylcarnitine and Glutarylcarnitine in stored blood spots. J Inherit Metab Dis. 2004;27(6):789-90.

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