H-HoPro-OH |
| カタログ番号GC31403 |
H-HoPro-OH (H-HoPro-OH) は、リジンの分解産物であり、ゼルウィガー症候群、新生児副腎白質ジストロフィーなどの全身性遺伝性ペルオキシソーム障害の乳児の体液に蓄積します。
Products are for research use only. Not for human use. We do not sell to patients.
Cas No.: 3105-95-1
Sample solution is provided at 25 µL, 10mM.
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H-HoPro-OH is a breakdown product of lysine, accumulates in body fluids of infants with generalized genetic peroxisomal disorders, such as Zellweger syndrome, neonatal adrenoleukodystrophy.
[1]. Mihalik SJ, et al. Peroxisomal L-pipecolic acid oxidation is deficient in liver from Zellweger syndrome patients. Pediatr Res. 1989 May;25(5):548-52.
Average Rating: 5 (Based on Reviews and 7 reference(s) in Google Scholar.)
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