L-Homocitrulline (Synonyms: ε-Carbamyllysine, L-Epsilon-Amino-Carbamoyl-Lysine, L-Homocitrulline, NSC 27428) |
カタログ番号GC31587 |
L-ホモシトルリンは、尿素サイクル経路を介してホモアルギニノコハク酸を介してホモアルギニンに代謝され、その代謝異常はリジン尿タンパク質不耐症 (LPI) につながる可能性があります。
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Cas No.: 1190-49-4
Sample solution is provided at 25 µL, 10mM.
L-Homocitrulline is metabolized to homoarginine through homoargininosuccinate via the urea cycle pathway and its metabolic abnormality could lead to Lysinuric Protein Intolerance (LPI).
[1]. Kato T, et al. Homocitrullinuria and homoargininuria in lysinuric protein intolerance. J Inherit Metab Dis. 1989;12(2):157-61.
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