Isovaleryl-DL-carnitine-d9 (chloride) (Synonyms: CAR 5:0-d9, C5:0 Carnitine-d9, DL-Carnitine isovaleryl ester-d9, DL-Isovalerylcarnitine-d9) |
Katalog-Nr.GC52009 |
An internal standard for the quantification of isovaleryl-DL-carnitine
Products are for research use only. Not for human use. We do not sell to patients.
Cas No.: 2608872-54-2
Sample solution is provided at 25 µL, 10mM.
Isovaleryl-DL-carnitine-d9 is intended for use as an internal standard for the quantification of isovaleryl-DL-carnitine by GC- or LC-MS. Isovaleryl-DL-carnitine is a derivative of carnitine . Increased levels of isovaleryl carnitine are associated with isovaleric acidemia, an inborn error of metabolism characterized by a deficiency in isovaleryl-CoA dehydrogenase.1
1.Rinaldo, P., Cowan, T.M., and Matern, D.Acylcarnitine profile analysisGenet.Med.10(2)151-156(2008)
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